Primary coronary artery anomalies include ectopic left or right artery departure from the opposite coronary sinus, left coronary artery departure from the pulmonary artery and congenital coronary arteriovenous fistulas.
In the case of ectopic arterial departure, the diagnosis should include determining the site of the arterial outlet and its correlation with the aorta and pulmonary artery. Perfusion abnormalities should also be determined by scintigraphy or exercise-induced ventricular arrhythmias. In a left artery outflow, it is also necessary to determine the site of the left artery and its relationship to the right coronary artery, ventricular function and the mitral valve. In congenital coronary fistulas, its anatomy and the status of the coronary arteries and left ventricular function are important.
A number of investigations such as a clinical examination, ECG, chest X-ray, echocardiogram with Doppler to determine flows, Holter ECG, angiocardiography and cardiac catheterisation are performed to determine the above conditions. After undergoing appropriately selected treatment, it is necessary to undergo ongoing medical follow-up as recommended, but at least once every two years."[1]